Tetralogy of Fallot
Sinabi ng dati kong classmate na si Brian na merong Tetralogy of Fallot ang kanyang anak na babae na si Milo. Nag-usap kami habang nasa tindahan sa kabila ako at karga niya sa Milo. Milo is 8 years old female, grade 3, pero dahil sa present ng kanyang sakit, mukha siyang 2-3 years old.
Definition
Isa itong congenital heart disease na under ng cyanotic heart defects. It occurs 10% of children with congental heart diseases at common ang mga boys dito. Apat (tetra) ang anomalies nito: pulmonary stenosis, ventricular septal defect, overriding or dextroposition of aorta & right ventricular hypertrophy.

Etiology
Hereditary, exposure to rubella virus & failure of structure to
progress ang mga causes kung bakit nagkakaroon nito.
Clinical manifestation
Right ventricular hypertrophy, high degree cyanosis, polycythemia (mataas ang RBC), severe dyspnea, growth retardation, tet spell or blue (episode of hypoxia), syncope, clubbing of fingernails (d/t chronic tissue hypoxia), mental retardation, x-ray reveals boot-shaped heart
Management
-Oxygen therapy
-No valsalva maneuver (fiber diet, laxative)
-Morphine sulfate - for pain
-Propranolol (Inderal) - decrese heart spasm
-Palliative repair that includes Blalock-Taussig procedure (parang gagawa ng ductus arteriosus to oxygenate the blood. Dahil subclavian artery ang ginamit, walang pulse sa right arm ng bata after the procedure.) and Brock procedure (relieves of pulmonary stenosis, VSD and overriding of aorta)
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